RARE CAUSE OF PULMONARY HYPERTENSION : UNILATERAL ABSENCE OF PULMONARY ARTERY. A CASE SERIES

Abstract

Unilateral absent pulmonary artery (UAPA) is one of the rare congenital anomaly seen in adulthood1
.Unilateral
absence of pulmonary artery usually occurs with other congenital defects such as Tetrology of fallot or septal defects
but it can also occur as a isolated anomaly which is very rare. Isolated absence of pulmonary artery is a rare cause of
pulmonary hypertension.We report three cases of absent right pulmonary artery presenting with severe pulmonary
hypertesion. Diagnosis needs high index of clinical suspicion and close scrutiny of radiological investigations for the
diagnosis.