Abstract

Becker muscular dystrophy (BMD) is an inherited congenital muscular disorder caused due to mutation in the dystrophin gene. Clinical presentation includes progressive muscle loss and variable weakness involving primarily the proximal lower limb muscles. BMD has a milder disease course compared to Duchenne Muscular dystrophy; but as the disease progresses patients invariably develop cardiac failure and less commonly respiratory failure. Anaesthetic management of patients with BMD are challenging to the anaesthesiologist due to the risk of malignant hyperthermia, rhabdomyolysis, hyperkalaemia, cardiac arrhythmia and respiratory failure.

Description