Abstract

Granulomatosis with Polyangiitis (GPA), formerly known as Wegener's granulomatosis, is a rare systemic necrotizing vasculitis predominantly affecting small to medium-sized blood vessels, with a reported annual incidence of approximately 10-20 cases per million. The disease is often characterized by necrotizing granulomatous inflammation that can involve multiple organs, most commonly the lungs and kidneys. This case report presents an unusual instance of GPA with diffuse alveolar hemorrhage in an 18-year-old male, highlighting the importance of early diagnosis, comprehensive clinical evaluation, and multidisciplinary management in achieving optimal patient outcomes.

Description