Journal of Cardiovascular Disease Research
Anaesthetic Management of a sickle cell trait child with congenital insensitivity to pain and Anhidrosis: A case report.
Durga Kashyap Kosam , Smriti Bandhu , Ajay Kosam , Subhash Rawte
JCDR. 2024: 880-886
Abstract
Congenital insensitivity to pain with anhidrosis(CIPA) is extremely rarae autosomal recessive hereditary sensory neuropathy which affects pain sensation, thermoregulation and present with various degree of mental retardation.Due to its rare presentation anaesthetic management of such patients pose a challenge for Anaesthesiologists. In India very few cases have been reported till date. We are hereby reporting a case of 9 year old girl having sickle cell trait with CIPA posted for sequestrectomy of right Ankle.
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