Abstract

Persistent Mullerian duct syndrome is a rare condition occasionally encountered in men with normal phenotype but with presence of Mullerian duct structures. In India, owing to neglect and lack of facilities, we encounter this condition in adult males. A patient came with abdominal pain and subsequent work up done and they found a mass retroperitoneally and did a biopsy for the same. Biopsy proved it as a malignant pathology and the patient was started on chemotherapy to reduce the size of tumour. The patient undergone surgery after 6 months as it is a proven case of germ cell tumour. Though rare, every surgeon operating upon inguinal hernia or undescended testes or cryptorchidism needs to know about the presence of the uterus in a phenotypic male patient at any age. High degree of suspicion and awareness is needed to diagnose this condition. We report successful anaesthetic management of a 29-year-old male with persistent mullerian duct syndrome scheduled for exploratory laparotomy under general anaesthesia with epidural catheter insertion for intraoperative and postoperative pain management

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