Abstract

Hemangioblastoms are benign tumors that primarily occur in the central nervous system (CNS). They account for approximately 1.5-2.5% of all brain tumors and 7-12% of infratentorial tumors in adults. The most frequent association of hemangioblastoms is with von Hippel-Lindau (VHL) syndrome, which is characterised by a chromosomal mutation on 3p. In cases of VHL syndrome, these tumors can be found in various locations both within and outside the CNS. On the other hand, sporadic solitary hemangioblastoms, although uncommon, are typically limited to the posterior cranial fossa. The primary treatment option for these tumors is complete surgical removal, making surgery the preferred and most effective approach

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