Abstract

The aim of the study is to study the clinical profile of patients with sickle cell disease between 01 to 18 years of age at a tertiary care center. A detailed history was elicited from parents and patients and clinical examination was done. The risk factors associated, clinical and investigation details, treatment received was noted. Patients diagnosed as sickle cell disease through appropriate laboratory techniques were registered for detail clinical assessment and follow up. The most common clinical features in sickle cell diseases were considered fever (82.9%), followed by pain, pain were classified as abdominal pain (29.2%), chest pain (53.65%), Pain over limb (hand & foot syndrome) (70.7%) and average duration of pain was three days. (17.07%) were founding limping & dyspnea (24.39%) & 65.29% were found to have jaundice during the sickle cell anemia episode. Most of the sickle cell anemia were frequently associated with anemia.

Description